TABLE 2. Onconeural antibodies

Antibody

# patients reported

Identified by more that one laboratory

Paraneoplastic neurological syndrome

Tumors

% of antibody positive patients without cancer 1 (# of patients studied)

Frecuency in isolated cancer

(# studied)

Anti-Yo (PCA1)

>200

Yes

Paraneoplastic cerebellar degeneration (PCD) 

Ovary, breast

4% (125)

1% (107)

Anti-Hu (ANNA1)

>600

Yes

Sensory neuronopathy 

Encephalomyelitis 

Chronic pseudoobstruction  

PCD 

Limbic encephalitis 

Small-cell lung cancer (SCLC)

2% (200)

16% (196) (1% with titers similar to those patients with PNS)

Anti-CV2(CRMP5)

>100

Yes

Chorea 

Sensory neuronopathy 

Sensorimotor neuropathy 

Encephalomyelitis 

Chronic pseudoobstruction  

PCD 

Limbic encephalitis 

SCLC, thymoma

4% (47)

9% (74)

Anti-Ri (ANNA2)

 50

Yes

Brainstem encephalitis 

Breast, SCLC

9% (22)

4% (181 ovarian cancer)

Anti-Ma2

18

Yes

Limbic/mesodiencephalic encephalitis 

Testicular

0% (18)

0% (175)

Anti-amphiphysin

13

Yes

Stiff-person syndrome 

Various syndromes  

Breast

SCLC

0% (10)

 

0% (25 breast, ovary)

1%(146 SCLC)

Anti-Tr (PCA-Tr)

28

Yes

PCD 

Hodgkin’s disease

11% (28)

0% (30)

Anti-Ma

11

Yes

Brainstem encephalitis/PCD 

Various tumors

10% (11)

0% (175)

Anti-ANNA3

11

No

Various syndromes  

SCLC

9% (11)

?

Anti-PCA2

9

No

Various syndromes 

SCLC

0% (8)

2% (58)

Anti-Zic

8

No

PCD 

SCLC

12% (8)

16% (74)

Anti-mGluR1

2

No

PCD 

Hodgkin’s disease

50% (2)

?

1 Defined by number of patients with follow-up of more than 3 years and no tumor found